A case of systemic scleroderma complicating pulmonary hypertension

[A case of systemic scleroderma complicating pulmonary hypertension].

The patient was a 7-year-old girl. At the age of 6, deposits of pigment had appeared on the skin of her face and limbs, the skin had become sclerosed, and she had developed dyspnea on exertion. Her previous physician had hospitalized her. She was diagnosed as systemic scleroderma that accompanied pulmonary hypertension by her symptoms and laboratory findings. She was referred to our hospital at...

Pulmonary Hypertension Complicating Systemic Hypertension, Is Diastolic Dysfunction the Culprit?

Background: Elevation in PA pressures has been observed by 2D echo in some but not all hypertensive patients. The mechanism and hemodynamic impact of pulmonary hypertension in these patients remains unclear. Methods: We reviewed echoes of all patients referred with systemic hypertension between 9/2006 to 5/2009 to identify those patients with left ventricular hypertrophy, normal systolic functi...

Idiopathic portal hypertension complicating systemic sclerosis: a case report

BACKGROUND Patients with systemic sclerosis may develop mild abnormalities of liver function tests. More serious hepatic involvement has been well documented but is rare. Idiopathic portal hypertension had been reported only in a few female patients with systemic sclerosis. CASE PRESENTATION An 82-year-old man with known systemic sclerosis presented with melaena. Urgent gastroscopy revealed o...

Pulmonary hypertension complicating pulmonary sarcoidosis

Pulmonary hypertension (PH) is a severe complication of sarcoidosis, with an unknown prevalence. The aetiology is multifactorial, and the exact mechanism of PH in the individual patient is often difficult to establish. The diagnostic work-up and treatment of PH in sarcoidosis is complex, and should therefore be determined by a multidisciplinary expert team in a specialised centre. It is still a...

Idiopathic portal hypertension complicating systemic sclerosis: Case report